It's one of the rare condition ..
It is characterized by asymptomatic subcutaneous mass which enlarges gradually. Sometimes pruritus or ulcers may be accompanying symptoms.
Sites: head and neck region most commonly affected.
Others: trunk or extremities and sometimes inguinal or epitrochlear lymph nodes.
Superficial glands may be affected: parotid or submandibular gland
It's mostly solitary or can be multiple in number.
IgE and eosinophils are increased in such patients.
Renal system is affected with nephrotic syndrome presentation..
Differential diagnosis :
Lipoma
Subcutaneous tumor
Angiolymphoid hyperplasia with eosinophilia
Histopathology:
Cellular : increased eosinophils and follicular hyperplasia
Vascular : arborizing vascular proliferation of post capillary venules
Fibrocollagenous
Treatment :
Radical excision is first line therapy
Radiotherapy is second line
If multiple masses chemotherapy is preferred
If renal involvement steroids is the first choice.
Recurrence is possible at primary site or other sites.
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Parotid swelling with subcutaneous swelling on arm |
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